Background & Aims Alagille syndrome is a genetic disorder characterized by cholestasis,
ocular abnormalities, characteristic facial features, heart defects, and vertebral …

Objective This review aims to highlight the clinicopathological characteristics and differential
diagnosis of central hepatic regenerative nodules (CHRNs) in patients with Alagille …

Abstract Background Children with Alagille syndrome undergo surveillance radiologic
examinations as they are at risk for developing cirrhosis and hepatocellular carcinoma …

Alagille syndrome (AGS) is a developmental, multiorgan disease caused by mutations of the
Jagged1 gene. The liver is one of the major organs affected in AGS, and the hallmark of liver …

Background: Hepatic lesions have been described in Alagille syndrome (ALGS) in isolated
case reports, and most of these have been reported to be hepatocellular carcinoma …

Introduction Alagille syndrome is a multisystem autosomal disorder. The main clinical
features are chronic cholestasis due to paucity of intrahepatic bile ducts, which can progress …

A boy with Alagille syndrome complicated by hepatic nodular hyperplasia (HNH) is reported.
During pre-transplantation evaluation, CT and MRI revealed a large hepatic lesion with …

Alagille syndrome (ALGS) is a complex, multisystem disease associated with mutations in
the JAG1 gene. In the liver, ALGS is characterized by paucity of intrahepatic bile ducts. Gene …

PURPOSE: To determine the anatomy of the portal venous system in the posterior aspect of
segment IV of the liver by using helical computed tomography (CT) during arterial …

Background Published case series have described central hepatic macroregenerative
nodules or masses as a common feature of Alagille syndrome. Our experience suggests this …