Clinical Characteristics and IgG4-RD Involvement
| Patient | ||||||
| No. | Age | Sex | Biopsy site | Treatment | Serum IgG4 (mg/L) | Involvement of IgG4-RD |
| 1 | 21 | M | Pancreas | Prednisone, MMF | 29,300 | Pituitary stalk, lacrimal gland, salivary gland, lung, pleura, pericardium, liver, gallbladder, pancreas, prostate, LN |
| 2 | 58 | M | Parotid | None | 11,300 | Salivary gland, lung, pancreas, prostate, LN |
| 3 | 52 | M | Gallbladder | None | 71,700 | Lacrimal gland, salivary gland, intrahepatic bile duct, pancreas, prostate, LN |
| 4 | 56 | M | Lacrimal gland | Prednisone | 14,600 | Lacrimal gland, extraocular muscle, salivary gland, pleura, pancreas, periaortitis, peritoneum, LN |
| 5 | 60 | M | None | None | 14,400 | Lacrimal gland, salivary gland, pancreas |
| 6 | 59 | F | Pancreas | None | 11,700 | Lacrimal gland, salivary gland, pancreas, LN |
| 7 | 24 | F | None | None | 3,510 | Retroperitoneal fibrosis |
| 8 | 55 | M | Pancreas | None | 34,100 | Lacrimal gland, salivary gland, intrahepatic bile duct, liver, pancreas, prostate, LN |
| 9 | 62 | M | Lacrimal gland | None | 27,900 | Lacrimal gland, salivary gland, nasal cavity, pleura, prostate, seminal vesicle, peritoneum, LN |
| 10 | 63 | M | None | None | 1,530 | Retroperitoneal fibrosis, LN |
| 11 | 17 | M | Submandibular gland, pancreas | None | 1,380 | Salivary gland, pancreas |
| 12 | 42 | F | Lung | Prednisone | 355 | Lacrimal gland, salivary gland, lung |
| 13 | 55 | M | None | None | 21,600 | Lacrimal gland, salivary gland, lung, liver, pancreas, prostate, LN |
| 14 | 57 | M | None | None | 33,700 | Lacrimal gland, salivary gland, lung, pleura, periaortitis, pancreas, prostate, seminal vesicle, LN |
| 15 | 64 | M | LN, kidney | None | 28,200 | Nasal cavity, lung, pleura, intrahepatic bile duct, pancreas, periaortitis, kidney, prostate, LN |
| 16 | 63 | F | Submandibular gland, LN | None | 47,200 | Lacrimal gland, salivary gland, lung, pancreas, LN |
| 17 | 63 | M | Submandibular gland | None | 73,400 | Lacrimal gland, salivary gland, nasal cavity, lung, intrahepatic bile duct, pancreas, LN |
| 18 | 40 | M | None | None | 6,710 | Pancreas, kidney, LN |
| 19 | 51 | M | Pancreas | Prednisone | 34,500 | Salivary gland, pancreas, kidney |
| 20 | 57 | M | None | Prednisone, MMF | 54,400 | Lacrimal gland, salivary gland, pancreas, kidney |
| 21 | 59 | F | None | None | 3,370 | Retroperitoneal fibrosis, LN |
| 22 | 55 | M | None | None | 3,210 | Salivary gland, pancreas |
| 23 | 63 | M | Pancreas | None | 11,900 | Lacrimal gland, salivary gland, pancreas, prostate, LN |
| 24 | 45 | M | Pancreas | Prednisone, sirolimus, MMF | 1,730 | Pancreas |
| 25 | 50 | F | Lung | Prednisone | 580 | Salivary gland, lung, pleura |
| 26 | 47 | M | Retroperitoneal mass | None | 31,100 | Kidney and perirenal masses, peritoneum and retroperitoneal mass, seminal vesicle |
MMF = mycophenolate mofetil; LN = lymph node.