Patient no. | Sex | Genotype | Age (y) | Tumor location | Status | Maximum tumor diameter (cm) | Biochemical phenotype |
1 | M | NF1 | 66 | LA | Primary | 1.2 | E + NE |
2 | F | NF1 | 31 | LA | Primary | 4.0 | E + NE |
3 | F | RET | 62 | LA | Primary | 3.4 | E + NE |
4 | F | RET | 20 | RA | Primary | 3.5 | E + NE |
5 | M | RET | 35 | RA | Primary | 2.1 | E + NE |
6 | M | RET | 70 | LA | Primary | 3.0 | E |
7 | F | SDHA | 63 | LA | Primary | NA | NE + DA |
EA (thoracic spine) | Metastatic | NA | NE + DA | ||||
EA (paraaortic lymph node) | Metastatic | NA | NE + DA | ||||
8 | M | SDHA | 35 | EA (retroaortic lymph node) | Metastatic | NA | DA |
9 | M | SDHB | 46 | EA (dorsolateral bladder) | Recurrent | NA | NE + DA |
10 | M | SDHD | 64 | RA | Primary | 1.5 | NE + DA |
11 | M | VHL | 48 | RA | Primary | 2.2 | NE |
12 | F | Sporadic | 55 | LA | Primary | 11.0 | E + NE |
13 | F | Sporadic | 34 | RA | Primary | 5.0 | E + NE |
14 | M | Sporadic | 51 | EA (retrocaval lymph node) | Metastatic | 2.0 | NE |
15 | F | Sporadic | 33 | LA | Primary | 4.0 | E + NE |
16 | F | Sporadic | 56 | EA (paraaortic lymph node) | Primary | 1.4 | NE |
17 | M | Sporadic | 66 | LA | Primary | 1.8 | E |
18 | M | Sporadic | 85 | RA | Primary | NA | NE |
19 | M | Sporadic | 55 | LA | Primary | 3.5 | E + NE |
20 | M | Sporadic | 43 | LA | Primary | 10.0 | E + NE |
21 | F | Sporadic | 73 | LA | Primary | 12.5 | NE + DA |
22 | F | Sporadic | 55 | RA | Primary | 1.5 | E |
23 | M | Sporadic | 64 | RA | Primary | 5.0 | E + NE |
24 | F | Sporadic | 55 | LA | Primary | 6.0 | E + NE |
LA = left adrenal; RA = right adrenal; EA = extraadrenal; NA = not available; E = epinephrine; NE = norepinephrine; DA = dopamine.