Analysis According to Number of Affected Organ Systems
| No. of systems | Alive (n) | Dead (n) | Alive (%) | Mean age at diagnosis (y) | Median survival (mo) |
| 1 | 5 | 7 | 41.7 | 60.8 (SD, 9.4) | 97 (95% CI, 23–NA) |
| 2 | 6 | 15 | 28.6 | 60.0 (SD, 10.6) | 81 (95% CI, 41–127) |
| 3, 4 | 3 | 8 | 27.3 | 59.3 (SD, 14.8) | 23 (95% CI, 18–NA) |
NA = not applicable.