Genotype | No. of patients | Sex (M/F) | Age (y) | Tumor location (adrenal/extraadrenal) | Maximum tumor diameter (cm) |
Sporadic | 33 | 10/23 | 45.0 ± 14.8 | 30/4 | 5.2 ± 2.9 |
SDHA | 1 | 0/1 | 19.0 | 1/0 | 8.0 |
SDHB | 2 | 1/1 | 30.0 ± 22.6 | 0/2 | 5.7 ± 1.0 |
SDHD | 4 | 2/2 | 44.0 ± 16.2 | 1/4 | 3.4 ± 1.2 |
VHL | 2 | 1/1 | 24.0 ± 13.9 | 1/2 | 2.2 ± 0.6 |
Multiple endocrine neoplasia type II | 12 | 8/4 | 49.0 ± 12.1 | 14/0 | 3.8 ± 2.4 |
NF1 | 2 | 0/2 | 48.0 ± 15.6 | 1/1 | 5.3 ± 2.4 |
MAX | 1 | 1/0 | 57.0 | 1/0 | 1.8 |
Study included 57 patients with 62 PPGLs. Data are expressed as mean ± SD.