Patients Characteristics
| Sex | Tumor location | ||||||
| Genotype | No. of patients | M | F | Age (y) | Adrenal | Extraadrenal | Tumor dimensions (cm3) |
| Sporadic* | 15 | 8 | 7 | 54.2 ± 14.9 | 14 | 1 | 47.9 ± 56.3 |
| SDHB | 2 | 2 | 0 | 31.0 ± 14.1 | 0 | 2 | 3.4 ± 2.4 |
| SDHD | 3 | 2 | 1 | 49.5 ± 13.4 | 1 | 2 | 26.0 ± 33.8 |
| MEN-2 | 5 | 4 | 1 | 46.8 ± 14.4 | 5 | 0 | 14.8 ± 21.0 |
| NF1 | 1 | 0 | 1 | 70 | 1 | 0 | 51.7 |
| MAX | 1 | 1 | 0 | 63 | 1 | 0 | 20.4 |
↵* Presence of germline mutations and large deletions in SDHB/C/D, RET, VHL, and—since 2011—in SHDA, SDHAF2, TMEM127, and MAX was investigated using standard procedures, and no mutation was detected.
Study included a total of 27 patients. Data are presented as mean ± SD.