Characteristics of Patients with Proven Pheochromocytomas or Paragangliomas (n = 68)
Characteristic | n |
Age (y) | |
Median | 42 |
Range | 7–80 |
Sex | |
Male | 41 (60) |
Female | 27 (40) |
Site of analyzed lesion | |
Adrenal | 27 (40) |
Head and neck | 20 (29) |
Other extraadrenal | 21 (31) |
Lesion | |
Primary | 45 (66) |
Multiple | 15 (22) |
Metastatic | 8 (12) |
Tumor size (cm) | |
<3 | 39 (57) |
3–6 | 19 (28) |
>6 | 6 (9) |
Not assessed | 4 (6) |
Scanner | |
ECAT 921 | 4 |
ECAT 922 | 49 |
PET/CT | 15 |
Mutation | |
VHL | 19 (28) |
SDHB | 12 (18) |
SDHC | 1 (1) |
SDHD | 8 (12) |
NF1 | 1 (1) |
RET | 1 (1) |
No mutation | 20 (29) |
Unknown | 6 (9) |
Gold standard | |
Histology | 36 (53) |
MRI | 25 (37) |
CT | 6 (9) |
DOTATATE PET | 1 (1) |
Data in parentheses are percentages.