Clinical Profile of 15 Patients with HI
Patient no. | Sex | Birth weight (g) | Gestational age (wk) | Age (mo) | Weight at PET scan (g) | Response to medication | Surgery | ||
---|---|---|---|---|---|---|---|---|---|
At diagnosis | At PET scan | ||||||||
1 | M | 3,470 | 36 | Neonatal | 5 | 7,500 | Dzx−, Octr− | Yes | |
2 | M | 3,760 | 40 | Neonatal | 3 | 5,800 | Dzx−, Octr− | Yes | |
3 | F | 3,310 | 38 | Neonatal | 2 | 5,000 | Dzx−, Octr− | Yes | |
4 | M | 3,871 | 38 | Neonatal | 4 | 9,160 | Dzx−, Octr− | Yes | |
5 | M | 4,050 | 37 | Neonatal | 7 | 10,870 | Dzx−, Octr+ | Yes | |
6 | M | 4,450 | 38 | Neonatal | 4 | 8,190 | Dzx−, Octr− | Yes | |
7 | M | 3,690 | 36 | Neonatal | 5 | 8,600 | Dzx−, Octr+ | No | |
8 | M | 3,900 | 39 | Neonatal | 3 and 12 | 6,800 | Dzx−, Octr+ | No | |
10,680 | |||||||||
9 | F | 2,950 | 37 | 2.5 | 13 | 11,000 | Dzx+ | No | |
10 | F | 4,010 | 37 | Neonatal | 8 | 7,300 | Dzx−, Octr+ | No | |
11 | F | 3,480 | 37 | Neonatal | 5 | 6,070 | Dzx−, Octr− | Yes | |
12 | M | 5,000 | 38 | Neonatal | 14 and 17 | 11,500 | Dzx−, Octr− | Yes | |
12,200 | |||||||||
13 | M | 3,700 | 38 | Neonatal | 2 | 6,670 | Dzx−, Octr+ | No | |
14 | M | 3,800 | 38 | Neonatal | 9 | 9,800 | Dzx−, Octr+ | No | |
15 | M | 3,580 | 36 | Neonatal | 2 | 6,000 | Dzx−, Octr− | Yes |
Dzx = diazoxide; Octr = octreotide.