TABLE 1

Clinical Profile of 15 Patients with HI

Patient no.SexBirth weight (g)Gestational age (wk)Age (mo)Weight at PET scan (g)Response to medicationSurgery
At diagnosisAt PET scan
1M3,47036Neonatal57,500Dzx−, Octr−Yes
2M3,76040Neonatal35,800Dzx−, Octr−Yes
3F3,31038Neonatal25,000Dzx−, Octr−Yes
4M3,87138Neonatal49,160Dzx−, Octr−Yes
5M4,05037Neonatal710,870Dzx−, Octr+Yes
6M4,45038Neonatal48,190Dzx−, Octr−Yes
7M3,69036Neonatal58,600Dzx−, Octr+No
8M3,90039Neonatal3 and 126,800Dzx−, Octr+No
10,680
9F2,950372.51311,000Dzx+No
10F4,01037Neonatal87,300Dzx−, Octr+No
11F3,48037Neonatal56,070Dzx−, Octr−Yes
12M5,00038Neonatal14 and 1711,500Dzx−, Octr−Yes
12,200
13M3,70038Neonatal26,670Dzx−, Octr+No
14M3,80038Neonatal99,800Dzx−, Octr+No
15M3,58036Neonatal26,000Dzx−, Octr−Yes
  • Dzx = diazoxide; Octr = octreotide.