TABLE 3

Classification of Osteosarcoma

Classification%
Primary high-grade, intramedullary75
 Mixed pattern (73%)
 Bone rich/sclerosing (9%)
 Cartilage rich (5%)
 Spindle cell rich
 Malignant histiocyte rich
 Telangiectatic
 Small cell rich (Ewing-like)
 Benign giant cell rich
 Epitheloid cell rich
Primary low-grade, intramedullary4–5
 Fibrous dysplasia-like (50%)
 Nonossifying fibroma-like (25%)
 Osteoblastoma-like (15%)
 Chondromyxoid fibroma-like (10%)
Secondary intramedullary6
Multifocal1–2
Intracortical0.2
Juxtacortical7–10
 Parosteal (65%)
 Periosteal (25%)
 High-grade surface (10%)
Osteosarcoma of jaw6
  • Classification according to Mirra (1).