TABLE 4

Etiologic Classification of Lymphedema

Primary lymphedemaSecondary lymphedema
CongenitalParasitic (filariasis)
Familial (Milroy’s disease)Postsurgical (lymph node dissection, after vascular surgery)
Syndrome associated (Turner’s, Klippel-Trénaunay, Noonan’s, etc.)Postinfectious
SporadicPost-traumatic
PrecoxMalignant (secondary to tumor obstruction of nodes)
 Familial (Meige’s disease)Lymphedema complicating chronic venous insufficiency
 Sporadic
Tarda