TABLE 1.

Clinical Features of Patients with Langerhans' Cell Histiocytosis

Patient no.Age (y)SexHistiocytosis typeOrgans involvedDelay from diagnosis (y)Biopsy provenLung CT scan
144MMultifocalLungs, bones, cerebellum, soft tissues14YesCystic lesions
240FUnifocalLungs3YesCystic lesions
329MMultifocalLungs, skin, salivary glands, pituitary gland7YesCystic lesions
427FUnifocalLungs1YesCystic lesions
543MUnifocalLungs18YesCystic lesions
645MUnifocalLungs3YesCystic lesions
731FUnifocalLungs1YesPredominantly nodules
852MMultifocalLungs, pituitary gland33YesCystic lesions
927MUnifocalLungs0.5NoNodules, cystic lesions
1030MMultifocalLungs, skin, salivary glands, pituitary gland, brain stem, liver9YesCystic lesions
1134FUnifocalLungs1YesNodules, cystic lesions
1235MUnifocalLungs0.3NoPredominantly nodules
1361FMultifocalBones2YesNormal